张琪;李玲义;张金龙;薛庆亮;

• 1:中国人民解放军兰州总医院呼吸内科

摘要(Abstract)：

肺毛细血管瘤病(PCH)是一种罕见的肺组织内血管增生性疾病,主要病理表现为大量薄壁毛细血管增生并浸润肺泡壁、气道、血管甚至胸膜,偶可侵及纵隔及心包,且增生的毛细血管常沿肺泡壁排列并包绕甚至压迫肺血管,可导致肺小静脉内膜增厚和肺小动脉血管重塑等,患者预后多不良。本文报道了1例PCH患者并复习相关文献以分析其可能的发病机制及诊治要点,以提高临床对该病的认识,减少误诊、漏诊。

关键词(KeyWords)： 血管瘤,毛细管;肺疾病;历史文献;病例报告

Abstract:

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作者(Author): 张琪;李玲义;张金龙;薛庆亮;

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参考文献(References)：

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